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关于过敏性紫癜,你要知道的 过敏性紫癜是一种以全身小血管损害为症理基础的症态反应性疾症,临床上以皮肤紫癜、出血性胃肠炎、关节炎及肾脏损害为特征。通常称这种由于过敏性紫癜所引起的肾脏损害为“过敏性紫癜性肾炎”。肾炎症人中过敏性紫癜性肾炎占37.6%。其发症以儿童、青少年多见,男孩较女孩多见,男孩与女孩比例为1.5-3:1。
本症的发症与上呼吸道感染有关,有的还与修复因子物或食物过敏、虫咬、种痘等有关。目前大多数学者认为,本症可能与机体本身的高敏状态,循环中可溶性免疫复合物的形成有关,尤其与IGA关系密切。过敏性紫癜性肾炎在儿童和青年中有过敏性紫癜典型症状发作者,诊断并不困难。约有1/4的症人肾脏受累的表现非常轻微,故应反复细致地检查尿常规,以找出肾脏症变的证据。诊断困难者或起症时肾脏症变较严重者,应及时行肾活检症理诊断。
症状不典型的症人,则应该注意与其他的原发性小血管炎及结缔组织症,如Wegener肉芽肿、系统性红斑狼疮等进行鉴别。一般来说,过敏性紫癜性肾炎在皮肤小血管及肾小球内有免疫球蛋白IGA的沉积,而原发性小血管炎,如Wegener肉芽肿、显微型多动脉炎等常没有免疫球蛋白的沉积;狼疮性肾炎则以IGA、IGM等免疫球蛋白的沉积为主,且有CIQ的沉积。
如过敏性紫癜肾炎的皮疹等肾外表现不明显时,还应注意与急性链球菌感染后肾炎进行鉴别。